E75 — Disorders of sphingolipid metabolism and other lipid storage disorders
Is E75 billable?
No — E75 is a non-billable header code. E75 groups more specific codes and cannot be submitted on a claim. A valid ICD-10-CM code must be reported at the highest level of specificity available in its branch. Select one of the 26 billable codes beneath E75.
Billable codes under this header
- E75.3Sphingolipidosis, unspecified
- E75.4Neuronal ceroid lipofuscinosis
- E75.5Other lipid storage disorders
- E75.6Lipid storage disorder, unspecified
- E75.00GM2 gangliosidosis, unspecified
- E75.01Sandhoff disease
- E75.02Tay-Sachs disease
- E75.09Other GM2 gangliosidosis
- E75.10Unspecified gangliosidosis
- E75.11Mucolipidosis IV
- E75.19Other gangliosidosis
- E75.21Fabry (-Anderson) disease
- E75.22Gaucher disease
- E75.23Krabbe disease
- E75.25Metachromatic leukodystrophy
- E75.26Sulfatase deficiency
- E75.27Pelizaeus-Merzbacher disease
- E75.28Canavan disease
- E75.29Other sphingolipidosis
- E75.240Niemann-Pick disease type A
- E75.241Niemann-Pick disease type B
- E75.242Niemann-Pick disease type C
- E75.243Niemann-Pick disease type D
- E75.244Niemann-Pick disease type A/B
- E75.248Other Niemann-Pick disease
- E75.249Niemann-Pick disease, unspecified
E75 at a glance
| Code | E75 |
|---|---|
| Description | Disorders of sphingolipid metabolism and other lipid storage disorders |
| Billable | No — header code |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Excludes1 — never code together
The conditions below can never be reported together with E75 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E75 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E75 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E75, but a patient may have both at the same time. When documentation supports it, E75 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
What codes fall under E75? (7)
How long has E75 existed?
E75 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
Which codes are confused with E75?
ICD-10-CM declares these codes mutually exclusive with E75 — exactly one of each pair can be correct for a given encounter.