ICDcodes.org
FY2027

E75.242Niemann-Pick disease type C

Billable

Is E75.242 billable?

Yes — E75.242 is billable for FY2027. E75.242 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E75.242 may be submitted for encounters from October 1, 2026 through September 30, 2027.

E75.242 at a glance

CodeE75.242
DescriptionNiemann-Pick disease type C
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E75.242 group to?

E75.242 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

How is E75.242 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E75.242. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Niemann-Pick disease or syndrometypeC

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E75.242 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E75.242 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes1 — never code together — inherited from E75

The conditions below can never be reported together with E75.242 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)

Excludes1 — never code together — inherited from E75.2

The conditions below can never be reported together with E75.242 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • adrenoleukodystrophy [Addison-Schilder] (E71.528)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E75.242, but a patient may have both at the same time. When documentation supports it, E75.242 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E75.242 existed?

E75.242 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E75.242?

What other codes are in the E75.24 family? (6)