Q87 — Other specified congenital malformation syndromes affecting multiple systems
Is Q87 billable?
No — Q87 is a non-billable header code. Q87 groups more specific codes and cannot be submitted on a claim. A valid ICD-10-CM code must be reported at the highest level of specificity available in its branch. Select one of the 21 billable codes beneath Q87.
Billable codes under this header
- Q87.0Congenital malformation syndromes predominantly affecting facial appearance
- Q87.2Congenital malformation syndromes predominantly involving limbs
- Q87.3Congenital malformation syndromes involving early overgrowth
- Q87.5Other congenital malformation syndromes with other skeletal changes
- Q87.ALoeys-Dietz syndrome
- Q87.11Prader-Willi syndrome
- Q87.19Other congenital malformation syndromes predominantly associated with short stature
- Q87.40Marfan syndrome, unspecified
- Q87.42Marfan syndrome with ocular manifestations
- Q87.43Marfan syndrome with skeletal manifestation
- Q87.81Alport syndrome
- Q87.82Arterial tortuosity syndrome
- Q87.83Bardet-Biedl syndrome
- Q87.84Laurence-Moon syndrome
- Q87.85MED13L syndrome
- Q87.86Kleefstra syndrome
- Q87.87Hao-Fountain Syndrome
- Q87.88CTNNB1 syndrome
- Q87.89Other specified congenital malformation syndromes, not elsewhere classified
- Q87.410Marfan syndrome with aortic dilation
- Q87.418Marfan syndrome with other cardiovascular manifestations
Q87 at a glance
| Code | Q87 |
|---|---|
| Description | Other specified congenital malformation syndromes affecting multiple systems |
| Billable | No — header code |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Use additional code
Report an additional code alongside Q87 to fully describe the condition. Q87 is sequenced first.
- code(s) to identify all associated manifestations
Excludes2 — not included here — inherited from Chapter 17
The conditions below are not part of Q87, but a patient may have both at the same time. When documentation supports it, Q87 and the excluded code may both be reported.
- inborn errors of metabolism (E70-E88)
What codes fall under Q87? (8)
- Q87.0Congenital malformation syndromes predominantly affecting facial appearance
- Q87.1Congenital malformation syndromes predominantly associated with short staturenot billable
- Q87.2Congenital malformation syndromes predominantly involving limbs
- Q87.3Congenital malformation syndromes involving early overgrowth
- Q87.4Marfan syndromenot billable
- Q87.5Other congenital malformation syndromes with other skeletal changes
- Q87.8Other specified congenital malformation syndromes, not elsewhere classifiednot billable
- Q87.ALoeys-Dietz syndrome
How long has Q87 existed?
Q87 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
Which codes are confused with Q87?
ICD-10-CM declares these codes mutually exclusive with Q87 — exactly one of each pair can be correct for a given encounter.