E75.240 — Niemann-Pick disease type A
Is E75.240 billable?
Yes — E75.240 is billable for FY2027. E75.240 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E75.240 may be submitted for encounters from October 1, 2026 through September 30, 2027.
E75.240 at a glance
| Code | E75.240 |
|---|---|
| Description | Niemann-Pick disease type A |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does E75.240 group to?
E75.240 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 642Inborn and Other Disorders of Metabolismmedical
How is E75.240 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to E75.240. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Deficiency, deficient › infantile neurovisceral acid sphingomyelinase
- Niemann-Pick disease or syndrome › type › A
- Deficiency, deficient › acid sphingomyelinase › type › A
Inclusion terms
Alternative wording in documentation that is classified to E75.240.
- Acid sphingomyelinase deficiency type A (ASMD type A)
- Infantile neurovisceral acid sphingomyelinase deficiency
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E75.240 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E75.240 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from E75
The conditions below can never be reported together with E75.240 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from E75.2
The conditions below can never be reported together with E75.240 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- adrenoleukodystrophy [Addison-Schilder] (E71.528)
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E75.240, but a patient may have both at the same time. When documentation supports it, E75.240 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
How long has E75.240 existed?
E75.240 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.