ICD-10 Code for Niemann-Pick Disease or Syndrome
The ICD-10-CM code for Niemann-Pick Disease or Syndrome is E75.249 — Niemann-Pick disease, unspecified. This is the code the Alphabetic Index gives for Niemann-Pick Disease or Syndrome with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
E75.249 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which Niemann-Pick Disease or Syndrome code should you use?
The Alphabetic Index lists 7 codes under Niemann-Pick disease or syndrome. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| specified NEC | E75.248 | Other Niemann-Pick disease |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources