Q87.A — Loeys-Dietz syndrome

BillableCCNew in FY2027

Is Q87.A billable?

Yes — Q87.A is billable for FY2027. Q87.A is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. Q87.A may be submitted for encounters from October 1, 2026 through September 30, 2027. Q87.A is new in FY2027.

Q87.A at a glance

Code	Q87.A
Description	Loeys-Dietz syndrome
Billable	Yes
Code set	ICD-10-CM FY2027
Valid for encounters	October 1, 2026 – September 30, 2027
FY2027 change	New in FY2027

Which MS-DRGs does Q87.A group to?

Q87.A sits in MDC 08 and helps define the logic of 3 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

564Other Musculoskeletal System and Connective Tissue Diagnoses with MCCmedical
565Other Musculoskeletal System and Connective Tissue Diagnoses with CCmedical
566Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCCmedical

As a secondary diagnosis, Q87.A is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is Q87.A listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to Q87.A. They show the wording a clinician may have documented, which often differs from the Tabular description.

Syndrome › Loeys-Dietz

Excludes1 — never code together

The conditions below can never be reported together with Q87.A on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

arterial tortuosity syndrome (Q87.82)
Ehlers-Danlos syndrome (Q79.6)
Marfan syndrome (Q87.40-Q87.43)
other systemic involvement of connective tissue (M35)

Use additional code — inherited from Q87

Report an additional code alongside Q87.A to fully describe the condition. Q87.A is sequenced first.

code(s) to identify all associated manifestations

Excludes2 — not included here — inherited from Chapter 17

The conditions below are not part of Q87.A, but a patient may have both at the same time. When documentation supports it, Q87.A and the excluded code may both be reported.

inborn errors of metabolism (E70-E88)

Which codes are confused with Q87.A?

ICD-10-CM declares these codes mutually exclusive with Q87.A — exactly one of each pair can be correct for a given encounter.