Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
Is Q87.89 billable?
Yes, but Q87.89 is an unspecified code. Q87.89 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, Q87.89 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting Q87.89 — the more specific alternatives are listed below.
Q87.89 at a glance
| Code | Q87.89 |
|---|---|
| Description | Other specified congenital malformation syndromes, not elsewhere classified |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does Q87.89 group to?
Q87.89 sits in MDC 08 and helps define the logic of 3 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 564Other Musculoskeletal System and Connective Tissue Diagnoses with MCCmedical
- 565Other Musculoskeletal System and Connective Tissue Diagnoses with CCmedical
- 566Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCCmedical
As a secondary diagnosis, Q87.89 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.
How is Q87.89 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to Q87.89. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Birt-Hogg-Dube syndrome
- Cantrell's syndrome
- Cerebro-hepato-renal syndrome
- Syndrome › basal cell nevus
- Syndrome › Birt-Hogg-Dube syndrome
- Syndrome › cardiofaciocutaneous
- Syndrome › Glass
- Syndrome › Gorlin's
- Syndrome › Oliver-McFarlane
- Syndrome › SATB2-associated
- Syndrome › Snyder-Robinson
- Web, webbed › popliteal syndrome (congenital)
Excludes1 — never code together — inherited from Q87.8
The conditions below can never be reported together with Q87.89 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- Zellweger syndrome (E71.510)
Use additional code — inherited from Q87
Report an additional code alongside Q87.89 to fully describe the condition. Q87.89 is sequenced first.
- code(s) to identify all associated manifestations
Excludes2 — not included here — inherited from Chapter 17
The conditions below are not part of Q87.89, but a patient may have both at the same time. When documentation supports it, Q87.89 and the excluded code may both be reported.
- inborn errors of metabolism (E70-E88)
How long has Q87.89 existed?
Q87.89 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.