Excludes1 pair

Q79.6- vs Q87.A

Q79.6 and Q87.A are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on Q87.A
Ehlers-Danlos syndrome (Q79.6)
Q79.6

Ehlers-Danlos syndromes

Not billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q65-Q79
Indexed under
  • Syndrome › Meekeren-Ehlers-Danlos
Q87.A

Loeys-Dietz syndrome

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q80-Q89
Indexed under
  • Syndrome › Loeys-Dietz

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027