E88.1 — Lipodystrophy, not elsewhere classified
Is E88.1 billable?
No — E88.1 is a non-billable header code. E88.1 groups more specific codes and cannot be submitted on a claim. A valid ICD-10-CM code must be reported at the highest level of specificity available in its branch. Select one of the 6 billable codes beneath E88.1.
E88.1 at a glance
| Code | E88.1 |
|---|---|
| Description | Lipodystrophy, not elsewhere classified |
| Billable | No — header code |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Excludes1 — never code together
The conditions below can never be reported together with E88.1 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- Whipple's disease (K90.81)
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E88.1 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E88.1 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from E88
The conditions below can never be reported together with E88.1 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- histiocytosis X (chronic) (C96.6)
Use additional code — inherited from E88
Report an additional code alongside E88.1 to fully describe the condition. E88.1 is sequenced first.
- codes for associated conditions
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E88.1, but a patient may have both at the same time. When documentation supports it, E88.1 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
What codes fall under E88.1? (6)
How long has E88.1 existed?
E88.1 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
- FY2026: E88.1 stopped being billable
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
What other codes are in the E88 family? (7)
- E88.0Disorders of plasma-protein metabolism, not elsewhere classifiednot billable
- E88.2Lipomatosis, not elsewhere classified
- E88.3Tumor lysis syndrome
- E88.4Mitochondrial metabolism disordersnot billable
- E88.8Other specified metabolic disordersnot billable
- E88.9Metabolic disorder, unspecified
- E88.AWasting disease (syndrome) due to underlying condition