D81.819 — Biotin-dependent carboxylase deficiency, unspecified
Is D81.819 billable?
Yes, but D81.819 is an unspecified code. D81.819 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, D81.819 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting D81.819 — the more specific alternatives are listed below.
More specific alternatives
D81.819 at a glance
| Code | D81.819 |
|---|---|
| Description | Biotin-dependent carboxylase deficiency, unspecified |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does D81.819 group to?
D81.819 sits in MDC 10 and helps define the logic of 2 MS-DRGs (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 640Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes with MCCmedical
- 641Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes without MCCmedical
How is D81.819 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to D81.819. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Deficiency, deficient › biotin-dependent carboxylase
- Immunodeficiency › combined › biotin-dependent carboxylase
Inclusion terms
Alternative wording in documentation that is classified to D81.819.
- Multiple carboxylase deficiency, unspecified
Excludes1 — never code together — inherited from D80-D89
The conditions below can never be reported together with D81.819 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from D81
The conditions below can never be reported together with D81.819 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
Excludes1 — never code together — inherited from D81.81
The conditions below can never be reported together with D81.819 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
Excludes2 — not included here — inherited from Chapter 3
The conditions below are not part of D81.819, but a patient may have both at the same time. When documentation supports it, D81.819 and the excluded code may both be reported.
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Excludes2 — not included here — inherited from D80-D89
The conditions below are not part of D81.819, but a patient may have both at the same time. When documentation supports it, D81.819 and the excluded code may both be reported.
- human immunodeficiency virus [HIV] disease (B20)
How long has D81.819 existed?
D81.819 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.