D81.810 — Biotinidase deficiency
Is D81.810 billable?
Yes — D81.810 is billable for FY2027. D81.810 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. D81.810 may be submitted for encounters from October 1, 2026 through September 30, 2027.
D81.810 at a glance
| Code | D81.810 |
|---|---|
| Description | Biotinidase deficiency |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does D81.810 group to?
D81.810 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 642Inborn and Other Disorders of Metabolismmedical
How is D81.810 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to D81.810. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Deficiency, deficient › biotinidase
- Immunodeficiency › combined › biotin-dependent carboxylase › biotinidase
Excludes1 — never code together — inherited from D80-D89
The conditions below can never be reported together with D81.810 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from D81
The conditions below can never be reported together with D81.810 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
Excludes1 — never code together — inherited from D81.81
The conditions below can never be reported together with D81.810 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
Excludes2 — not included here — inherited from Chapter 3
The conditions below are not part of D81.810, but a patient may have both at the same time. When documentation supports it, D81.810 and the excluded code may both be reported.
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Excludes2 — not included here — inherited from D80-D89
The conditions below are not part of D81.810, but a patient may have both at the same time. When documentation supports it, D81.810 and the excluded code may both be reported.
- human immunodeficiency virus [HIV] disease (B20)
How long has D81.810 existed?
D81.810 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.