ICD-10 Code for Von Willebrand Disease (VWD)
The ICD-10-CM code for von Willebrand disease (VWD) is D68.00 — Von Willebrand disease, unspecified. It is billable for FY2027.
Von Willebrand disease ICD-10 codes at a glance
| Condition | Von Willebrand disease (VWD) |
|---|---|
| Code | D68.00 — Von Willebrand disease, unspecified |
| Billable | Yes (D68.00) |
| Alphabetic Index entry | Disease, diseased, von Willebrand |
| Code set | ICD-10-CM FY2027, valid October 1, 2026 – September 30, 2027 |
What changes the von Willebrand disease code?
The Alphabetic Index lists these qualifiers under Disease, diseased, von Willebrand. If the record documents one of them, the code changes. Verify the code in the Tabular List before reporting it.
| acquired | D68.04 | Acquired von Willebrand disease |
| platelet-type | D68.09 | Other von Willebrand disease |
| pseudo | D68.09 | Other von Willebrand disease |
| specified NEC | D68.09 | Other von Willebrand disease |
| type 1 | D68.01 | Von Willebrand disease, type 1 |
| type 1C | D68.01 | Von Willebrand disease, type 1 |
| type 2 | D68.029 | Von Willebrand disease, type 2, unspecified |
| type 2 › type 2A | D68.020 | Von Willebrand disease, type 2A |
| type 2 › type 2B | D68.021 | Von Willebrand disease, type 2B |
| type 2 › type 2M | D68.022 | Von Willebrand disease, type 2M |
| type 2 › type 2N | D68.023 | Von Willebrand disease, type 2N |
| type 3 | D68.03 | Von Willebrand disease, type 3 |
What else changes the von Willebrand disease code?
The type documented changes the code: type 1 (D68.01), type 2 with its subtype 2A/2B/2M/2N specified or unspecified (D68.020–D68.029), type 3 (D68.03), or acquired von Willebrand disease (D68.04), coded separately from the inherited types 1–3.
What does the Tabular List say about D68.00?
The instructional notes that govern D68.00, including those it inherits from its category and chapter. An Excludes1 note means the two codes are never reported together.
Excludes1 — never code together — inherited from D68
The conditions below can never be reported together with D68.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- abnormal coagulation profile NOS (R79.1)
Excludes1 — never code together — inherited from D68.0
The conditions below can never be reported together with D68.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes2 — not included here — inherited from Chapter 3
The conditions below are not part of D68.00, but a patient may have both at the same time. When documentation supports it, D68.00 and the excluded code may both be reported.
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Excludes2 — not included here — inherited from D68
The conditions below are not part of D68.00, but a patient may have both at the same time. When documentation supports it, D68.00 and the excluded code may both be reported.
Codes, descriptions and Index entries are from the official ICD-10-CM FY2027 release. Guideline text is quoted from the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027. A code must always be verified in the Tabular List before it is reported. Data sources