ICD-10 Code for Sjögren Syndrome
Also searched as Sjögren's syndrome, sjogrens syndrome
The ICD-10-CM code for sjögren syndrome is M35.00 — Sjogren syndrome, unspecified. It is billable for FY2027.
Sjögren syndrome ICD-10 codes at a glance
| Condition | Sjögren syndrome |
|---|---|
| Code | M35.00 — Sjogren syndrome, unspecified |
| Billable | Yes (M35.00) |
| Alphabetic Index entry | Syndrome, Sjögren |
| Code set | ICD-10-CM FY2027, valid October 1, 2026 – September 30, 2027 |
What changes the sjögren syndrome code?
The Alphabetic Index lists these qualifiers under Syndrome, Sjögren. If the record documents one of them, the code changes. Verify the code in the Tabular List before reporting it.
| with › central nervous system involvement | M35.07 | Sjogren syndrome with central nervous system involvement |
| with › dental involvement | M35.0C | Sjogren syndrome with dental involvement |
| with › gastrointestinal involvement | M35.08 | Sjogren syndrome with gastrointestinal involvement |
| with › glomerular disease | M35.0A | Sjogren syndrome with glomerular disease |
| with › inflammatory arthritis | M35.05 | Sjogren syndrome with inflammatory arthritis |
| with › keratoconjunctivitis | M35.01 | Sjogren syndrome with keratoconjunctivitis |
| with › lung involvement | M35.02 | Sjogren syndrome with lung involvement |
| with › myopathy | M35.03 | Sjogren syndrome with myopathy |
| with › peripheral nervous system involvement | M35.06 | Sjogren syndrome with peripheral nervous system involvement |
| with › renal tubular acidosis | M35.04 | Sjogren syndrome with tubulo-interstitial nephropathy |
| with › specified organ involvement, NEC | M35.09 | Sjogren syndrome with other organ involvement |
| with › tubulo-interstitial nephropathy | M35.04 | Sjogren syndrome with tubulo-interstitial nephropathy |
| with › vasculitis | M35.0B | Sjogren syndrome with vasculitis |
What else changes the sjögren syndrome code?
M35.00 is used only when no organ complication is documented. A separate code identifies keratoconjunctivitis, lung, renal, articular, neurologic or other organ involvement when the record specifies it.
What does the Tabular List say about M35.00?
The instructional notes that govern M35.00, including those it inherits from its category and chapter. An Excludes1 note means the two codes are never reported together.
Excludes1 — never code together — inherited from M30-M36
The conditions below can never be reported together with M35.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Excludes1 — never code together — inherited from M35
The conditions below can never be reported together with M35.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- reactive perforating collagenosis (L87.1)
Excludes1 — never code together — inherited from M35.0
The conditions below can never be reported together with M35.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- dry mouth, unspecified (R68.2)
Use additional code — inherited from M35.0
Report an additional code alongside M35.00 to fully describe the condition. M35.00 is sequenced first.
- code to identify associated manifestations
Excludes2 — not included here — inherited from Chapter 13
The conditions below are not part of M35.00, but a patient may have both at the same time. When documentation supports it, M35.00 and the excluded code may both be reported.
- arthropathic psoriasis (L40.5-)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- compartment syndrome (traumatic) (T79.A-)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Codes, descriptions and Index entries are from the official ICD-10-CM FY2027 release. Guideline text is quoted from the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027. A code must always be verified in the Tabular List before it is reported. Data sources