ICD-10 Code for Marfan Syndrome

The ICD-10-CM code for marfan syndrome is Q87.40 — Marfan syndrome, unspecified. It is billable for FY2027.

Q87.40 billableUnspecified

Marfan syndrome ICD-10 codes at a glance

ConditionMarfan syndrome
CodeQ87.40 — Marfan syndrome, unspecified
BillableYes (Q87.40)
Alphabetic Index entrySyndrome, Marfan
Code setICD-10-CM FY2027, valid October 1, 2026 – September 30, 2027

What changes the marfan syndrome code?

The Alphabetic Index lists these qualifiers under Syndrome, Marfan. If the record documents one of them, the code changes. Verify the code in the Tabular List before reporting it.

with › cardiovascular manifestationsQ87.418Marfan syndrome with other cardiovascular manifestations
with › ocular manifestationsQ87.42Marfan syndrome with ocular manifestations
with › skeletal manifestationsQ87.43Marfan syndrome with skeletal manifestation

What else changes the marfan syndrome code?

Q87.40 is used when no manifestation is documented. A separate code identifies cardiovascular (Q87.41-, including aortic dilation specifically at Q87.410), ocular (Q87.42) or skeletal (Q87.43) manifestations when the record specifies them.

What does the Tabular List say about Q87.40?

The instructional notes that govern Q87.40, including those it inherits from its category and chapter. An Excludes1 note means the two codes are never reported together.

Use additional code — inherited from Q87

Report an additional code alongside Q87.40 to fully describe the condition. Q87.40 is sequenced first.

  • code(s) to identify all associated manifestations

Excludes2 — not included here — inherited from Chapter 17

The conditions below are not part of Q87.40, but a patient may have both at the same time. When documentation supports it, Q87.40 and the excluded code may both be reported.

  • inborn errors of metabolism (E70-E88)

Codes, descriptions and Index entries are from the official ICD-10-CM FY2027 release. Guideline text is quoted from the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027. A code must always be verified in the Tabular List before it is reported. Data sources