Which cardiomyopathy code should you use?
The Alphabetic Index lists 33 codes under Cardiomyopathy. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| alcoholic | I42.6 | Alcoholic cardiomyopathy |
| amyloid | E85.4 | Organ-limited amyloidosis |
| arrhythmogenic | I42.81 | Arrhythmogenic cardiomyopathy |
| beriberi | E51.12 | Wet beriberi |
| cobalt-beer | I42.6 | Alcoholic cardiomyopathy |
| congenital | I42.4 | Endocardial fibroelastosis |
| congestive | I42.00 | Dilated cardiomyopathy, unspecified |
| constrictive NOS | I42.5 | Other restrictive cardiomyopathy |
| dilated | I42.00 | Dilated cardiomyopathy, unspecified |
| glycogen storage | E74.02 | Pompe disease |
| hypertrophic | I42.2 | Other hypertrophic cardiomyopathy |
| ischemic | I25.5 | Ischemic cardiomyopathy |
| metabolic | E88.9 | Metabolic disorder, unspecified |
| newborn | I42.89 | Other cardiomyopathies not elsewhere classified |
| non-ischemic | I42.89 | Other cardiomyopathies not elsewhere classified |
| nutritional | E63.9 | Nutritional deficiency, unspecified |
| obscure of Africa | I42.89 | Other cardiomyopathies not elsewhere classified |
| peripartum | O90.3 | Peripartum cardiomyopathy |
| postpartum | O90.3 | Peripartum cardiomyopathy |
| restrictive NEC | I42.5 | Other restrictive cardiomyopathy |
| rheumatic | I09.0 | Rheumatic myocarditis |
| secondary | I42.9 | Cardiomyopathy, unspecified |
| specified NEC | I42.89 | Other cardiomyopathies not elsewhere classified |
| stress induced | I51.81 | Takotsubo syndrome |
| takotsubo | I51.81 | Takotsubo syndrome |
| thyrotoxic | E05.90 | Thyrotoxicosis, unspecified without thyrotoxic crisis or storm |
| toxic NEC | I42.7 | Cardiomyopathy due to drug and external agent |
| transthyretin-related familial amyloid | E85.4 | Organ-limited amyloidosis |
| tuberculous | A18.84 | Tuberculosis of heart |
| viral | B33.24 | Viral cardiomyopathy |
Cardiomyopathy amyloid
| transthyretin-related familial | E85.4 | Organ-limited amyloidosis |
Cardiomyopathy arrhythmogenic
| biventricular | I42.81 | Arrhythmogenic cardiomyopathy |
| ventricular | I42.81 | Arrhythmogenic cardiomyopathy |
Cardiomyopathy dilated
| familial-genetic | I42.01 | Familial-genetic dilated cardiomyopathy |
| specified NEC | I42.09 | Other dilated cardiomyopathy |
Cardiomyopathy due to
| alcohol | I42.6 | Alcoholic cardiomyopathy |
| beriberi | E51.12 | Wet beriberi |
| cardiac glycogenosis | E74.02 | Pompe disease |
| drugs | I42.7 | Cardiomyopathy due to drug and external agent |
| external agents NEC | I42.7 | Cardiomyopathy due to drug and external agent |
| Friedreich's ataxia | G11.11 | Friedreich ataxia |
| myotonia atrophica | G71.11 | Myotonic muscular dystrophy |
| progressive muscular dystrophy | G71.09 | Other specified muscular dystrophies |
Cardiomyopathy hypertrophic
| obstructive | I42.1 | Obstructive hypertrophic cardiomyopathy |
| obstructive › congenital | Q24.8 | Other specified congenital malformations of heart |
Cardiomyopathy in
| Chagas' disease | B57.2 | Chagas' disease (chronic) with heart involvement |
| sarcoidosis | D86.85 | Sarcoid myocarditis |
| Chagas' disease › acute | B57.0 | Acute Chagas' disease with heart involvement |
Cardiomyopathy metabolic
| thyrotoxic | E05.90 | Thyrotoxicosis, unspecified without thyrotoxic crisis or storm |
| thyrotoxic › with thyroid storm | E05.91 | Thyrotoxicosis, unspecified with thyrotoxic crisis or storm |
Cardiomyopathy newborn
| congenital | I42.4 | Endocardial fibroelastosis |
Cardiomyopathy nutritional
Cardiomyopathy thyrotoxic
| with thyroid storm | E05.91 | Thyrotoxicosis, unspecified with thyrotoxic crisis or storm |