N01 — Rapidly progressive nephritic syndrome
Is N01 billable?
No — N01 is a non-billable header code. N01 groups more specific codes and cannot be submitted on a claim. A valid ICD-10-CM code must be reported at the highest level of specificity available in its branch. Select one of the 11 billable codes beneath N01.
Billable codes under this header
- N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
- N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
- N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
- N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N01.6Rapidly progressive nephritic syndrome with dense deposit disease
- N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
- N01.8Rapidly progressive nephritic syndrome with other morphologic changes
- N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes
- N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis
N01 at a glance
| Code | N01 |
|---|---|
| Description | Rapidly progressive nephritic syndrome |
| Billable | No — header code |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Excludes1 — never code together
The conditions below can never be reported together with N01 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- nephritic syndrome NOS (N05.-)
Includes
Conditions classified to N01.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Excludes1 — never code together — inherited from N00-N08
The conditions below can never be reported together with N01 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- hypertensive chronic kidney disease (I12.-)
Excludes2 — not included here — inherited from Chapter 14
The conditions below are not part of N01, but a patient may have both at the same time. When documentation supports it, N01 and the excluded code may both be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Code also — inherited from N00-N08
Two codes may be needed to describe the condition fully. Whether N01 is sequenced first depends on the reason for the encounter.
- any associated kidney failure (N17-N19).
What codes fall under N01? (11)
- N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
- N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
- N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
- N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N01.6Rapidly progressive nephritic syndrome with dense deposit disease
- N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
- N01.8Rapidly progressive nephritic syndrome with other morphologic changes
- N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes
- N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis
How long has N01 existed?
N01 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.