E78.010 — Homozygous familial hypercholesterolemia [HoFH]
Is E78.010 billable?
Yes — E78.010 is billable for FY2027. E78.010 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E78.010 may be submitted for encounters from October 1, 2026 through September 30, 2027.
E78.010 at a glance
| Code | E78.010 |
|---|---|
| Description | Homozygous familial hypercholesterolemia [HoFH] |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does E78.010 group to?
E78.010 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 642Inborn and Other Disorders of Metabolismmedical
How is E78.010 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to E78.010. They show the wording a clinician may have documented, which often differs from the Tabular description.
- HoFH (homozygous familial hypercholesterolemia)
- Cholesterolemia › familial › homozygous (essential) (pure)
- Hypercholesterolemia › familial › homozygous [HoFH] (essential) (primary) (pure)
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E78.010 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E78.010 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes1 — never code together — inherited from E78
The conditions below can never be reported together with E78.010 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- sphingolipidosis (E75.0-E75.3)
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E78.010, but a patient may have both at the same time. When documentation supports it, E78.010 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
How long has E78.010 existed?
E78.010 first appears in FY2026.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.