Excludes1 pair
E75.3 vs E78-
E75.3 and E78 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.
The official note, declared on E78
sphingolipidosis (E75.0-E75.3)
E75.3
Sphingolipidosis, unspecified
BillableUnspecified
- Chapter 4
- Endocrine, nutritional and metabolic diseases
- Section
- E70-E88
Indexed under
- Sphingolipidosis
- Sphingomyelinosis
- Degeneration, degenerative › brain › in › sphingolipidosis
E78
Disorders of lipoprotein metabolism and other lipidemias
Not billable
- Chapter 4
- Endocrine, nutritional and metabolic diseases
- Section
- E70-E88
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027