E74 vs E76.3
E74 and E76.3 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
The official note, declared on E74
mucopolysaccharidosis (E76.0-E76.3)
E74
Other disorders of carbohydrate metabolism
Not billable
- Chapter 4
- Endocrine, nutritional and metabolic diseases
- Section
- E70-E88
E76.3
Mucopolysaccharidosis, unspecified
BillableUnspecified
- Chapter 4
- Endocrine, nutritional and metabolic diseases
- Section
- E70-E88
Indexed under
- Mucopolysaccharidosis
- Cardiopathy › mucopolysaccharidosis
- Mucopolysaccharidosis › cardiopathy
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027