E76.3 — Mucopolysaccharidosis, unspecified
Is E76.3 billable?
Yes, but E76.3 is an unspecified code. E76.3 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, E76.3 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting E76.3 — the more specific alternatives are listed below.
E76.3 at a glance
| Code | E76.3 |
|---|---|
| Description | Mucopolysaccharidosis, unspecified |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does E76.3 group to?
E76.3 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 642Inborn and Other Disorders of Metabolismmedical
As a secondary diagnosis, E76.3 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.
How is E76.3 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to E76.3. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Mucopolysaccharidosis
- Cardiopathy › mucopolysaccharidosis
- Mucopolysaccharidosis › cardiopathy
Excludes1 — never code together — inherited from Chapter 4
The conditions below can never be reported together with E76.3 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
Excludes1 — never code together — inherited from E70-E88
The conditions below can never be reported together with E76.3 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Excludes2 — not included here — inherited from E70-E88
The conditions below are not part of E76.3, but a patient may have both at the same time. When documentation supports it, E76.3 and the excluded code may both be reported.
- Ehlers-Danlos syndromes (Q79.6-)
How long has E76.3 existed?
E76.3 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
Which codes are confused with E76.3?
ICD-10-CM declares these codes mutually exclusive with E76.3 — exactly one of each pair can be correct for a given encounter.