ICD-10 Code for Sarcoglycanopathy
The ICD-10-CM code for sarcoglycanopathy is G71.0340 — Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified. This is the code the Alphabetic Index gives for sarcoglycanopathy with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
G71.0340 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which sarcoglycanopathy code should you use?
The Alphabetic Index lists 4 codes under Sarcoglycanopathy. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| alpha | G71.0341 | Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction | |
| beta | G71.0342 | Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction | |
| delta | G71.0349 | Limb girdle muscular dystrophy due to other sarcoglycan dysfunction | |
| gamma | G71.0349 | Limb girdle muscular dystrophy due to other sarcoglycan dysfunction |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources