ICD-10 Code for Porphyria
Also indexed as (South African)
The ICD-10-CM code for porphyria is E80.20 — Unspecified porphyria. This is the code the Alphabetic Index gives for porphyria with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
E80.20 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which porphyria code should you use?
The Alphabetic Index lists 4 codes under Porphyria. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| acquired | E80.20 | Unspecified porphyria | |
| acute intermittent | E80.21 | Acute intermittent (hepatic) porphyria | |
| cutanea tarda | E80.1 | Porphyria cutanea tarda | |
| due to drugs | E80.20 | Unspecified porphyria | |
| erythropoietic | E80.0 | Hereditary erythropoietic porphyria | |
| hepatocutaneous type | E80.1 | Porphyria cutanea tarda | |
| secondary | E80.20 | Unspecified porphyria | |
| toxic NEC | E80.20 | Unspecified porphyria | |
| variegata | E80.20 | Unspecified porphyria |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources