ICD-10 Code for Menkes' disease or syndrome
The ICD-10-CM code for menkes' disease or syndrome is E83.09 — Other disorders of copper metabolism. This is the code the Alphabetic Index gives for menkes' disease or syndrome with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
Billable
Which menkes' disease or syndrome code should you use?
The Alphabetic Index lists 2 codes under Menkes' disease or syndrome. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| meaning maple-syrup-urine disease | E71.0 | Maple-syrup-urine disease |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources