ICD-10 Code for Ichthyosis
Also indexed as (congenital)
The ICD-10-CM code for ichthyosis is Q80.9 — Congenital ichthyosis, unspecified. This is the code the Alphabetic Index gives for ichthyosis with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
Q80.9 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which ichthyosis code should you use?
The Alphabetic Index lists 9 codes under Ichthyosis. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| acquired | L85.0 | Acquired ichthyosis | |
| fetalis | Q80.4 | Harlequin fetus | |
| hystrix | Q80.8 | Other congenital ichthyosis | |
| lamellar | Q80.2 | Lamellar ichthyosis | |
| lingual | K13.29 | Other disturbances of oral epithelium, including tongue | |
| palmaris and plantaris | Q82.8 | Other specified congenital malformations of skin | |
| simplex | Q80.0 | Ichthyosis vulgaris | |
| vera | Q80.8 | Other congenital ichthyosis | |
| vulgaris | Q80.0 | Ichthyosis vulgaris | |
| X-linked | Q80.1 | X-linked ichthyosis |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources