ICD-10 Code for Dermatopolymyositis
The ICD-10-CM code for dermatopolymyositis is M33.90 — Dermatopolymyositis, unspecified, organ involvement unspecified. This is the code the Alphabetic Index gives for dermatopolymyositis with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
M33.90 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which dermatopolymyositis code should you use?
The Alphabetic Index lists 17 codes under Dermatopolymyositis. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| amyopathic | M33.93 | Dermatopolymyositis, unspecified without myopathy | |
| in neoplastic disease | D49.9 | Neoplasm of unspecified behavior of unspecified site | |
| juvenile | M33.00 | Juvenile dermatomyositis, organ involvement unspecified | |
| specified NEC | M33.10 | Other dermatomyositis, organ involvement unspecified | |
| without myopathy | M33.93 | Dermatopolymyositis, unspecified without myopathy |
Dermatopolymyositis with
Dermatopolymyositis juvenile
| amyopathic | M33.03 | Juvenile dermatomyositis without myopathy | |
| without myopathy | M33.03 | Juvenile dermatomyositis without myopathy | |
| with › myopathy | M33.02 | Juvenile dermatomyositis with myopathy | |
| with › respiratory involvement | M33.01 | Juvenile dermatomyositis with respiratory involvement | |
| with › specified organ involvement NEC | M33.09 | Juvenile dermatomyositis with other organ involvement |
Dermatopolymyositis specified NEC
| amyopathic | M33.13 | Other dermatomyositis without myopathy | |
| myopathy | M33.12 | Other dermatomyositis with myopathy | |
| respiratory involvement | M33.11 | Other dermatomyositis with respiratory involvement | |
| specified organ involvement NEC | M33.19 | Other dermatomyositis with other organ involvement | |
| without myopathy | M33.13 | Other dermatomyositis without myopathy |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources