ICD-10 Code for Creutzfeldt-Jakob Disease or Syndrome
Also indexed as (with dementia)
The ICD-10-CM code for Creutzfeldt-Jakob Disease or Syndrome is A81.00 — Creutzfeldt-Jakob disease, unspecified. This is the code the Alphabetic Index gives for Creutzfeldt-Jakob Disease or Syndrome with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
A81.00 is billable but unspecified. If the documentation names a type, site or cause, one of the more specific codes below is likely expected.
Which Creutzfeldt-Jakob Disease or Syndrome code should you use?
The Alphabetic Index lists 3 codes under Creutzfeldt-Jakob disease or syndrome. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources