ICD-10 Code for Arnold-Chiari Disease, Obstruction or Syndrome
Also indexed as (type II)
The ICD-10-CM code for Arnold-Chiari Disease, Obstruction or Syndrome is Q07.00 — Arnold-Chiari syndrome without spina bifida or hydrocephalus. This is the code the Alphabetic Index gives for Arnold-Chiari Disease, Obstruction or Syndrome with no further qualifier, valid for FY2027 (October 1, 2026 – September 30, 2027).
Which Arnold-Chiari Disease, Obstruction or Syndrome code should you use?
The Alphabetic Index lists 5 codes under Arnold-Chiari disease, obstruction or syndrome. Which one applies depends on the qualifier documented in the record — the type, site, cause, or associated condition. Find the qualifier below, then verify the code in the Tabular List before using it.
By type
| type IV | Q04.8 | Other specified congenital malformations of brain |
Arnold-Chiari Disease, Obstruction or Syndrome with
| hydrocephalus | Q07.02 | Arnold-Chiari syndrome with hydrocephalus |
| spina bifida | Q07.01 | Arnold-Chiari syndrome with spina bifida |
| hydrocephalus › with spina bifida | Q07.03 | Arnold-Chiari syndrome with spina bifida and hydrocephalus |
| spina bifida › with hydrocephalus | Q07.03 | Arnold-Chiari syndrome with spina bifida and hydrocephalus |
Index terms and codes are reproduced from the official ICD-10-CM FY2027 release. The Alphabetic Index is a finding aid — a code must always be verified in the Tabular List before it is reported. Data sources