ICDcodes.org
FY2027

E78.6 — Lipoprotein deficiency

Billable

Is E78.6 billable?

Yes — E78.6 is billable for FY2027. E78.6 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E78.6 may be submitted for encounters from October 1, 2026 through September 30, 2027.

E78.6 at a glance

CodeE78.6
DescriptionLipoprotein deficiency
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E78.6 group to?

E78.6 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

How is E78.6 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E78.6. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Abetalipoproteinemia
  • Acanthocytosis
  • Analphalipoproteinemia
  • Bassen-Kornzweig disease or syndrome
  • Hypoalphalipoproteinemia
  • Hypobetalipoproteinemia (familial)
  • Hypolipoproteinemia (alpha) (beta)
  • Tangier disease
  • Deficiency, deficient › lecithin cholesterol acyltransferase
  • Deficiency, deficient › lipoprotein
  • Depressed › HDL cholesterol
  • Disease, diseased › Tangier

Inclusion terms

Alternative wording in documentation that is classified to E78.6.

  • Abetalipoproteinemia
  • Depressed HDL cholesterol
  • High-density lipoprotein deficiency
  • Hypoalphalipoproteinemia
  • Hypobetalipoproteinemia (familial)
  • Lecithin cholesterol acyltransferase deficiency
  • Tangier disease

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E78.6 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E78.6 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes1 — never code together — inherited from E78

The conditions below can never be reported together with E78.6 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • sphingolipidosis (E75.0-E75.3)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E78.6, but a patient may have both at the same time. When documentation supports it, E78.6 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E78.6 existed?

E78.6 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E78.6?

What other codes are in the E78 family? (9)