ICDcodes.org
FY2027

E74.00Glycogen storage disease, unspecified

BillableUnspecifiedCC

Is E74.00 billable?

Yes, but E74.00 is an unspecified code. E74.00 is a valid, billable ICD-10-CM code for encounters from October 1, 2026 through September 30, 2027. However, E74.00 is an unspecified or catch-all code. Payers apply additional scrutiny to unspecified codes and many deny them when the medical record supports a more specific option, so check the documentation before selecting E74.00 — the more specific alternatives are listed below.

E74.00 at a glance

CodeE74.00
DescriptionGlycogen storage disease, unspecified
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E74.00 group to?

E74.00 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, E74.00 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is E74.00 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E74.00. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Aglycogenosis
  • Disease, diseasedglycogen storage
  • Disease, diseasedglycogen storagegeneralized
  • Disordertubulo-interstitialglycogen storage disease (of)
  • Myopathyinglycogen storage disease
  • Nephritis, nephritictubulo-interstitialdue toglycogen storage disease (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E74.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E74.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes1 — never code together — inherited from E74

The conditions below can never be reported together with E74.00 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • diabetes mellitus (E08-E13)
  • hypoglycemia NOS (E16.2)
  • increased secretion of glucagon (E16.3)
  • mucopolysaccharidosis (E76.0-E76.3)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E74.00, but a patient may have both at the same time. When documentation supports it, E74.00 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E74.00 existed?

E74.00 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E74.00?

What other codes are in the E74.0 family? (6)