ICDcodes.org
FY2027

E71.1113-methylglutaconic aciduria

BillableCC

Is E71.111 billable?

Yes — E71.111 is billable for FY2027. E71.111 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E71.111 may be submitted for encounters from October 1, 2026 through September 30, 2027.

E71.111 at a glance

CodeE71.111
Description3-methylglutaconic aciduria
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E71.111 group to?

E71.111 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, E71.111 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is E71.111 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E71.111. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Disordermetabolism NOSamino-acidbranched chain3-methylglutaconic aciduria (of)

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E71.111 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E71.111 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E71.111, but a patient may have both at the same time. When documentation supports it, E71.111 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E71.111 existed?

E71.111 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

What other codes are in the E71.11 family? (2)