ICDcodes.org
FY2027

E71.110Isovaleric acidemia

BillableCC

Is E71.110 billable?

Yes — E71.110 is billable for FY2027. E71.110 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. E71.110 may be submitted for encounters from October 1, 2026 through September 30, 2027.

E71.110 at a glance

CodeE71.110
DescriptionIsovaleric acidemia
BillableYes
Code setICD-10-CM FY2027
Valid for encountersOctober 1, 2026 – September 30, 2027

Which MS-DRGs does E71.110 group to?

E71.110 sits in MDC 10 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.

  • 642Inborn and Other Disorders of Metabolismmedical

As a secondary diagnosis, E71.110 is a complication or comorbidity (CC), which can move a stay into a higher-paying DRG.

How is E71.110 listed in the Alphabetic Index?

These are the routes through the Alphabetic Index that lead to E71.110. They show the wording a clinician may have documented, which often differs from the Tabular description.

  • Isovaleric acidemia
  • Acidemiaisovaleric
  • Disorderisovaleric acidemia (of)
  • Disordermetabolism NOSamino-acidbranched chainisovaleric acidemia (of)

Excludes1 — never code together — inherited from Chapter 4

The conditions below can never be reported together with E71.110 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes1 — never code together — inherited from E70-E88

The conditions below can never be reported together with E71.110 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2 — not included here — inherited from E70-E88

The conditions below are not part of E71.110, but a patient may have both at the same time. When documentation supports it, E71.110 and the excluded code may both be reported.

  • Ehlers-Danlos syndromes (Q79.6-)

How long has E71.110 existed?

E71.110 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.

Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.

Which conditions are coded to E71.110?

What other codes are in the E71.11 family? (2)