D56.0 — Alpha thalassemia
Is D56.0 billable?
Yes — D56.0 is billable for FY2027. D56.0 is a valid, billable ICD-10-CM code at the highest level of specificity in its branch. D56.0 may be submitted for encounters from October 1, 2026 through September 30, 2027.
D56.0 at a glance
| Code | D56.0 |
|---|---|
| Description | Alpha thalassemia |
| Billable | Yes |
| Code set | ICD-10-CM FY2027 |
| Valid for encounters | October 1, 2026 – September 30, 2027 |
Which MS-DRGs does D56.0 group to?
D56.0 sits in MDC 15 and helps define the logic of 1 MS-DRG (version 44, FY2027). Which one a stay actually groups to also depends on procedures and secondary diagnoses.
- 791Prematurity with Major Problemsmedical
How is D56.0 listed in the Alphabetic Index?
These are the routes through the Alphabetic Index that lead to D56.0. They show the wording a clinician may have documented, which often differs from the Tabular description.
- Hb › Bart's disease (abnormal)
- Hemoglobin › H Constant Spring
- Thalassemia › alpha (anemia) (disease)
- Disease, diseased › hemoglobin or Hb › Bart's
- Disease, diseased › hemoglobin or Hb › H
- Disease, diseased › hemoglobin or Hb › H › Constant Spring
- Hydrops › fetalis › due to › alpha thalassemia
- Hydrops › newborn › due to › alpha thalassemia
Excludes1 — never code together
The conditions below can never be reported together with D56.0 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
Use additional code
Report an additional code alongside D56.0 to fully describe the condition. D56.0 is sequenced first.
- code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Inclusion terms
Alternative wording in documentation that is classified to D56.0.
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
Excludes1 — never code together — inherited from D56
The conditions below can never be reported together with D56.0 on the same claim. An Excludes1 note means the two conditions cannot occur in the same patient, so reporting both is a coding error.
- sickle-cell thalassemia (D57.4-)
Excludes2 — not included here — inherited from Chapter 3
The conditions below are not part of D56.0, but a patient may have both at the same time. When documentation supports it, D56.0 and the excluded code may both be reported.
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
How long has D56.0 existed?
D56.0 has been in ICD-10-CM since at least FY2016, the earliest fiscal year on record here.
Derived from the official order files for FY2016–FY2026. FY2017 and FY2020 publish no order file, so those years are not covered.
Which codes are confused with D56.0?
ICD-10-CM declares these codes mutually exclusive with D56.0 — exactly one of each pair can be correct for a given encounter.