Q99.1 vs R62
Q99.1 and R62 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
46, XX true hermaphrodite
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q90-Q99
- 46, XX with streak gonads
- 46, XY with streak gonads
- Pure gonadal dysgenesis
- Swyer syndrome
- Hermaphrodite, hermaphroditism › 46,XX with streak gonads (true)
- Hermaphrodite, hermaphroditism › 46,XY with streak gonads (true)
- Syndrome › Swyer
- Dysgenesis › gonadal › pure
Lack of expected normal physiological development in childhood and adults
- Chapter 18
- Symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified
- Section
- R50-R69
These two codes sit in different chapters of the Tabular List, which is usually the clearest signal that they describe different underlying processes rather than different degrees of the same one.
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027