FY2027
MenuClose
Excludes1 pair

Q77.6 vs Q87.1-

Q77.6 and Q87.1 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on Q87.1
Ellis-van Creveld syndrome (Q77.6)
Q77.6

Chondroectodermal dysplasia

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q65-Q79
Use when the record says
  • Ellis-van Creveld syndrome
Indexed under
  • Chondroectodermal dysplasia
  • Ellis-van Creveld syndrome (chondroectodermal dysplasia)
  • Disease, diseased › Ellis-van Creveld (chondroectodermal dysplasia)
  • Dysplasia › chondroectodermal
  • Syndrome › chondroectodermal dysplasia
Q87.1

Congenital malformation syndromes predominantly associated with short stature

Not billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q80-Q89

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027