ICDcodes.org
FY2027

Q74.1 vs Q87.2

Q74.1 and Q87.2 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.

The official note, declared on Q74.1
nail patella syndrome (Q87.2)
Q74.1

Congenital malformation of knee

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q65-Q79
Use when the record says
  • Congenital absence of patella
  • Congenital dislocation of patella
  • Congenital genu valgum
  • Congenital genu varum
  • Rudimentary patella
Indexed under
  • Absence › patella, congenital (of) (organ or part) (complete or partial)
  • Agenesis › patella
  • Anomaly, anomalous › knee (congenital) (unspecified type)
  • Anomaly, anomalous › patella (congenital) (unspecified type)
  • Bifid › patella (congenital)
Q87.2

Congenital malformation syndromes predominantly involving limbs

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q80-Q89
Use when the record says
  • Holt-Oram syndrome
  • Klippel-Trenaunay-Weber syndrome
  • Nail patella syndrome
  • Rubinstein-Taybi syndrome
  • Sirenomelia syndrome
  • Thrombocytopenia with absent radius [TAR] syndrome
  • VATER syndrome
Indexed under
  • Fong's syndrome (hereditary osteo-onychodysplasia)
  • Holt-Oram syndrome
  • Klippel-Trenaunaysyndrome (-Weber)
  • Mietens' syndrome
  • Onycho-osteodysplasia

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027