Excludes1 pair

Q61.3 vs Q61.4

Q61.3 and Q61.4 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on Q61.4
polycystic kidney disease (Q61.11-Q61.3)
Q61.3

Polycystic kidney, unspecified

BillableUnspecified
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q60-Q64
Indexed under
  • Nephritis, nephritic › polycystic
  • Polycystic › degeneration, kidney
  • Polycystic › kidney
  • Degeneration, degenerative › kidney › polycystic
  • Disease, diseased › kidney › polycystic
Q61.4

Renal dysplasia

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q60-Q64
Use when the record says
  • Multicystic dysplastic kidney
  • Multicystic kidney (development)
  • Multicystic kidney disease
  • Multicystic renal dysplasia
Indexed under
  • Multicystic kidney (development)
  • Dysplasia › kidney
  • Dysplasia › renal
  • Disease, diseased › kidney › multicystic
  • Dysplasia › kidney › multicystic

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027