Q56 vs Q99.1
Q56 and Q99.1 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
The official note, declared on Q56
46,XX true hermaphrodite (Q99.1)
Q56
Indeterminate sex and pseudohermaphroditism
Not billable
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q50-Q56
Q99.1
46, XX true hermaphrodite
Billable
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q90-Q99
Use when the record says
- 46, XX with streak gonads
- 46, XY with streak gonads
- Pure gonadal dysgenesis
Indexed under
- Swyer syndrome
- Hermaphrodite, hermaphroditism › 46,XX with streak gonads (true)
- Hermaphrodite, hermaphroditism › 46,XY with streak gonads (true)
- Syndrome › Swyer
- Dysgenesis › gonadal › pure
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027