Excludes1 pair

Q56- vs Q99.0

Q56 and Q99.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on Q56
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
Q56

Indeterminate sex and pseudohermaphroditism

Not billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q50-Q56
Q99.0

Chimera 46, XX/46, XY

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q90-Q99
Use when the record says
  • Chimera 46, XX/46, XY true hermaphrodite
Indexed under
  • Chimera 46,XX/46,XY
  • Hermaphrodite, hermaphroditism › 46,XX/46,XY
  • Hermaphrodite, hermaphroditism › chimera 46,XX/46,XY

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027