ICDcodes.org
FY2027

Q04.0 vs Q04.3

Q04.0 and Q04.3 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.

The official note, declared on Q04.3
congenital malformations of corpus callosum (Q04.0)
Q04.0

Congenital malformations of corpus callosum

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q00-Q07
Use when the record says
  • Agenesis of corpus callosum
Indexed under
  • Absence › corpus callosum (of) (organ or part) (complete or partial)
  • Agenesis › corpus callosum
  • Aplasia › corpus callosum
  • Hypoplasia, hypoplastic › corpus callosum
  • Malformation › corpus callosum (congenital)
Q04.3

Other reduction deformities of brain

Billable
Chapter 17
Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
Section
Q00-Q07
Use when the record says
  • Absence of part of brain
  • Agenesis of part of brain
  • Agyria
  • Aplasia of part of brain
  • Hydranencephaly
  • Hypoplasia of part of brain
  • Lissencephaly
  • Microgyria
Indexed under
  • Agyria
  • Hydrancephaly, hydranencephaly
  • Lissencephalia, lissencephaly
  • Microgyria (congenital)
  • Pachygyria

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027