Excludes1 pair
Q00.0 vs Q75-
Q00.0 and Q75 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.
The official note, declared on Q75
anencephaly (Q00.0)
Q00.0
Anencephaly
Billable
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q00-Q07
Use when the record says
- Acephaly
- Acrania
- Amyelencephaly
- Hemianencephaly
- Hemicephaly
Indexed under
- Acephalia, acephalism, acephalus, acephaly
- Acrania
- Amyelencephalus, amyelencephaly
- Anencephalus, anencephaly
- Hemianencephaly
Q75
Other congenital malformations of skull and face bones
Not billable
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q65-Q79
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027