ICDcodes.org
FY2027

N04.6 vs N04.A

N04.6 and N04.A can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.

The official note, declared on N04.A
Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6)
N04.6

Nephrotic syndrome with dense deposit disease

Billable
Chapter 14
Diseases of the genitourinary system
Section
N00-N08
Use when the record says
  • Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
  • Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2
Indexed under
  • Syndrome › nephrotic › with › dense deposit disease
  • Syndrome › nephrotic › with › C3 › glomerulopathy › with dense deposit disease
N04.A

Nephrotic syndrome with C3 glomerulonephritis

Billable
Chapter 14
Diseases of the genitourinary system
Section
N00-N08
Use when the record says
  • Nephrotic syndrome with C3 glomerulopathy
Indexed under
  • Syndrome › nephrotic › with › C3 › glomerulonephritis
  • Syndrome › nephrotic › with › C3 › glomerulopathy

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027