Excludes1 pair

L00 vs L26

L00 and L26 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on L26
Ritter's disease (L00)
L00

Staphylococcal scalded skin syndrome

Billable
Chapter 12
Diseases of the skin and subcutaneous tissue
Section
L00-L08
Use when the record says
  • Ritter's disease
Indexed under
  • Ritter's disease
  • Staphylococcal scalded skin syndrome
  • Dermatitis › Ritter's (exfoliativa)
  • Disease, diseased › Ritter's
  • Syndrome › staphylococcal scalded skin
L26

Exfoliative dermatitis

Billable
Chapter 12
Diseases of the skin and subcutaneous tissue
Section
L20-L30
Use when the record says
  • Hebra's pityriasis
Indexed under
  • Dermatitis › exfoliative, exfoliativa (generalized)
  • Dermatosis › exfoliativa
  • Hebra's › pityriasis
  • Pityriasis › Hebra's

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027