I89 vs Q82.0
I89 and Q82.0 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.
The official note, declared on I89
hereditary lymphedema (Q82.0)
I89
Other noninfective disorders of lymphatic vessels and lymph nodes
Not billable
- Chapter 9
- Diseases of the circulatory system
- Section
- I80-I89
Q82.0
Hereditary lymphedema
Billable
- Chapter 17
- Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
- Section
- Q80-Q89
Indexed under
- Meige-Milroy disease (chronic hereditary edema)
- Meige's syndrome
- Milroy's disease (chronic hereditary edema)
- Nonne-Milroy syndrome
- Pseudoelephantiasis neuroarthritica
These two codes sit in different chapters of the Tabular List, which is usually the clearest signal that they describe different underlying processes rather than different degrees of the same one.
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027