Excludes1 pair

I82.0 vs K76.5

I82.0 and K76.5 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on K76.5
Budd-Chiari syndrome (I82.0)
I82.0

Budd-Chiari syndrome

Billable
Chapter 9
Diseases of the circulatory system
Section
I80-I89
Use when the record says
  • Hepatic vein thrombosis
Indexed under
  • Budd-Chiari syndrome (hepatic vein thrombosis)
  • Block, blocked › hepatic vein
  • Chiari's › disease or syndrome (hepatic vein thrombosis)
  • Disease, diseased › Chiari's (hepatic vein thrombosis)
  • Embolism › hepatic (vein)
K76.5

Hepatic veno-occlusive disease

Billable
Chapter 11
Diseases of the digestive system
Section
K70-K77
Indexed under
  • Disease, diseased › liver › veno-occlusive

These two codes sit in different chapters of the Tabular List, which is usually the clearest signal that they describe different underlying processes rather than different degrees of the same one.

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027