Excludes1 pair

G21- vs G90.3

G21 and G90.3 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on G21
Shy-Drager syndrome (G90.3)
G21

Secondary parkinsonism

Not billable
Chapter 6
Diseases of the nervous system
Section
G20-G26
G90.3

Multi-system degeneration of the autonomic nervous system

Billable
Chapter 6
Diseases of the nervous system
Section
G89-G99
Use when the record says
  • Neurogenic orthostatic hypotension [Shy-Drager]
Indexed under
  • Shy-Drager syndrome
  • Degeneration, degenerative › multi-system
  • Hypotension › neurogenic, orthostatic
  • Parkinsonism › with neurogenic orthostatic hypotension (symptomatic)
  • Hypotension › orthostatic › neurogenic

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027