ICDcodes.org
FY2027

E25.0 vs E30.1

E25.0 and E30.1 can never be reported together. ICD-10-CM declares them mutually exclusive with an Excludes1 note, meaning the two conditions cannot occur in the same patient — so exactly one of them is correct for any given encounter.

The official note, declared on E30.1
congenital adrenal hyperplasia (E25.0)
E25.0

Congenital adrenogenital disorders associated with enzyme deficiency

Billable
Chapter 4
Endocrine, nutritional and metabolic diseases
Section
E20-E35
Use when the record says
  • Congenital adrenal hyperplasia
  • 21-Hydroxylase deficiency
  • Salt-losing congenital adrenal hyperplasia
Indexed under
  • Adrenogenitalism, congenital
  • Adrenogenital syndrome › congenital
  • Adrenogenital syndrome › salt loss
  • Defect, defective › 3-beta-hydroxysteroid dehydrogenase
  • Defect, defective › 11-hydroxylase
E30.1

Precocious puberty

Billable
Chapter 4
Endocrine, nutritional and metabolic diseases
Section
E20-E35
Use when the record says
  • Precocious menstruation
Indexed under
  • Precocity, sexual (constitutional) (cryptogenic) (female) (idiopathic) (male)
  • Pubarche, precocious
  • Pubertas praecox
  • Breast › buds
  • Buds › breast

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027