Excludes1 pair

D69.4- vs D82.0

D69.4 and D82.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on D69.4
Wiskott-Aldrich syndrome (D82.0)
D69.4

Other primary thrombocytopenia

Not billable
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D65-D69
D82.0

Wiskott-Aldrich syndrome

Billable
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D80-D89
Use when the record says
  • Immunodeficiency with thrombocytopenia and eczema
Indexed under
  • Aldrich (-Wiskott) syndrome (eczema-thrombocytopenia)
  • Wiskott-Aldrich syndrome
  • Syndrome › Aldrich (-Wiskott)
  • Syndrome › eczema-thrombocytopenia
  • Syndrome › familial eczema-thrombocytopenia (Wiskott-Aldrich)

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027