Excludes1 pair

D68.0- vs D69.8

D68.0 and D69.8 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on D68.0
capillary fragility (hereditary) (D69.8)
D68.0

Von Willebrand disease

Not billable
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D65-D69
D69.8

Other specified hemorrhagic conditions

BillableUnspecified
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Section
D65-D69
Use when the record says
  • Capillary fragility (hereditary)
  • Vascular pseudohemophilia
Indexed under
  • Endotheliosis (hemorrhagic infectional)
  • Fragile, fragility › capillary (hereditary)
  • Pseudohemophilia › Type A
  • Pseudohemophilia › vascular
  • Purpura › capillary fragility (hereditary) (idiopathic)

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027