Excludes1 pair
D66 vs D68.0-
D66 and D68.0 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.
The official note, declared on D68.0
factor VIII deficiency NOS (D66)
D66
Hereditary factor VIII deficiency
Billable
- Chapter 3
- Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
- Section
- D65-D69
Use when the record says
- Classical hemophilia
- Deficiency factor VIII (with functional defect)
- Hemophilia NOS
- Hemophilia A
Indexed under
- Hemophilia (classical) (familial) (hereditary)
- Subhemophilia
- Arthropathy › hemophilic NEC
- Disease, diseased › bleeder's
- Hemophilia › A
D68.0
Von Willebrand disease
Not billable
- Chapter 3
- Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
- Section
- D65-D69
Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027