Excludes1 pair

D33.0 vs D33.1

D33.0 and D33.1 are not coded together. ICD-10-CM declares them mutually exclusive with an Excludes1 note — the two conditions are not expected to occur together, so exactly one of them is normally correct for a given encounter. The Official Guidelines carve out one exception: if the two conditions are clearly unrelated to each other, both may be reported.

The official note, declared on D33.0
benign neoplasm of fourth ventricle (D33.1)
D33.0

Benign neoplasm of brain, supratentorial

Billable
Chapter 2
Neoplasms
Section
D10-D36
Use when the record says
  • Benign neoplasm of cerebral ventricle
  • Benign neoplasm of cerebrum
  • Benign neoplasm of frontal lobe
  • Benign neoplasm of occipital lobe
  • Benign neoplasm of parietal lobe
  • Benign neoplasm of temporal lobe
Indexed under
  • Papilloma › choroid plexus (lateral ventricle) (third ventricle)
D33.1

Benign neoplasm of brain, infratentorial

Billable
Chapter 2
Neoplasms
Section
D10-D36
Use when the record says
  • Benign neoplasm of brain stem
  • Benign neoplasm of cerebellum
  • Benign neoplasm of fourth ventricle
Indexed under
  • Papilloma › choroid plexus › fourth ventricle

Excludes1 is not always absolute: where two conditions covered by the note are genuinely unrelated, CMS guidance permits reporting both. Document the reasoning rather than assuming it. More on Excludes1 vs Excludes2 · FY2027